HEREDITARY GINGIVAL FIBROMATOSIS PDF

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Hereditary gingival fibromatosis (HGF), also known as idiopathic gingival hyperplasia, is a rare condition of gingival overgrowth. HGF is characterized as a . Hereditary, drug-induced, and idiopathic gingival overgrowth have been reported . Hereditary gingival fibromatosis can occur as an isolated. Mutation in SOS1, son-of-sevenless gene, is thought to be responsible for hereditary gingival fibromatosis. This report shows a case of.

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Hereditary Gingival Fibromatosis: A Review and a Report of a Rare Case

An unusual case report. However, in some cases where it can develop as a result of rare multi-system syndromes, such as: The HGF is classified in two types, nodular type and symmetric type.

HGF usually begins during the transition from primary to permanent teeth, giving rise to a condition that can have negative psychological effects at that age. J Am Dent Assoc. Am J Hum Genet ; The patient narrated that she often used to chew food with her gums and never used to practice oral hygiene measures. It may occur singly or in association with other inherited syndromes.

The mass in anterior palatine region had granular, mildly pigmented surface having pinkish white color. The symmetric form, which is the most common type of disorder, results in uniform enlargement of the gingiva that is firm, dense, resilient, insensitive fibrous tissue that covers the alveolar ridges and extends over the teeth resulting in extensive pseudo pockets.

This would cause an imbalance between the synthesis and degradation of extracellular matrix molecules 358 – The patient and her parents noticed gingival enlargement when she was seven years old with gradual spacing of teeth. The presented patient seemed to be a case of nonsyndromic HGF which the isolated nature of the condition was further confirmed by a physician.

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A Age of the patient: Periapical, mandibular and maxillary hard tissues — Bones of jaws Agnathia Alveolar osteitis Buccal exostosis Cherubism Idiopathic osteosclerosis Mandibular fracture Microgenia Micrognathia Intraosseous cysts Odontogenic: Subscribe to Table of Contents Alerts.

Gingival fibromatosis combined hereditarg cherubism and psychomotor retardation: Since this condition is generally agreed upon to be hereditarynothing can be done to prevent HGF.

Hereditary gingival fibromatosis – Wikipedia

This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3. This report presents the clinical features and the management of 12 year old female child with a severe variety of HGF. Mutations in the gene encoding capillary morphogenesis protein 2 cause juvenile hyaline fibromatosis and infantile systemic hyalinosis.

It can cover teeth in various degrees, and can lead to aesthetic disfigurement. Specialised Social Services Eurordis directory. How to cite this URL: Transforming growth factor-beta1 autocrine stimulation regulates fibroblast proliferation in hereditary gingival fibromatosis.

The histological findings are nonspecific and include acanthotic and hyperkeratotic epithelium tingival elongated rete ridges deeply extended to a relative avascular connective tissue with densely arranged collagen bundles and numerous fibroblasts [ 114 ]. The localized form usually affects the maxillary molar and tuberosity area, particularly on the palatal surface.

Hereditary gingival fibromatosis: Characteristics and treatment approach

Histochemical, immunohistochemical, and ultrastructural studies of gingival fibromatosis: The enlargement in our patient was particularly prominent in the anterior palate and mandibular anterior region. This article has been cited by other articles in PMC.

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Diagnoses Chronic periodontitis Localized aggressive periodontitis Generalized aggressive periodontitis Periodontitis as a heredktary of systemic disease Periodontosis Necrotizing periodontal diseases Abscesses of the periodontium Herrditary periodontic-endodontic lesions.

Periodontium gingivaperiodontal ligamentcementumalveolus — Gums and tooth-supporting structures. Case Reports -Case 1. Histomorphometric characteristics and expression of epidermal growth factor and its receptor by epithelial cells of normal gingiva and hereditary gingival fibromatosis.

Only comments written in English can be processed. HGF can appear on its own or as part of a syndrome 25. An occurrence of the disease has been found in two generations of this family and therefore, it may be following autosomal dominant trait of inheritance.

There was no history of consanguinity.

Hereditary gingival fibromatosis

This page was last edited on 20 Decemberat Upper anterior teeth were protruded and mandibular plane angle was large vertical growth pattern Figure 8. Both autosomal dominant and autosomal recessive modes of inheritance have been reported [ 3 — 5 ]. HGF usually involves the marginal gingiva, however only the interdental papilla involvement is also reported. In the patient presented, deferring orthodontic treatment until growth potential decreases and correcting the problem through combined orthodontic and orthognathic procedures were planned.